Incontinentia pigmenti (Bloch-Sulzberger syndrome): a case report.

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Data

1993-06-01

Autores

Niccoli-Filho, W. D.
da Rocha, J. C.
Di Nicoló, R.
Seraidarian, P. I.

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Resumo

A syndrome--incontinentia pigmenti--of probable genetic etiology, is discussed and a new case report presented. The syndrome presents systemic and dental manifestations, which are separate although similar to those found in other disease entities, i.e., congenital syphilis, hereditary ectodermal dysplasia.

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Palavras-chave

case report, child, female, human, incontinentia pigmenti, pathology, pathophysiology, sex difference, tooth eruption, tooth malformation, Case Report, Child, Female, Human, Incontinentia Pigmenti, Sex Factors, Tooth Abnormalities, Tooth Eruption

Como citar

The Journal of clinical pediatric dentistry, v. 17, n. 4, p. 251-253, 1993.

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