Incontinentia pigmenti (Bloch-Sulzberger syndrome): a case report.
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Data
1993-06-01
Autores
Niccoli-Filho, W. D.
da Rocha, J. C.
Di Nicoló, R.
Seraidarian, P. I.
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Resumo
A syndrome--incontinentia pigmenti--of probable genetic etiology, is discussed and a new case report presented. The syndrome presents systemic and dental manifestations, which are separate although similar to those found in other disease entities, i.e., congenital syphilis, hereditary ectodermal dysplasia.
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Palavras-chave
case report, child, female, human, incontinentia pigmenti, pathology, pathophysiology, sex difference, tooth eruption, tooth malformation, Case Report, Child, Female, Human, Incontinentia Pigmenti, Sex Factors, Tooth Abnormalities, Tooth Eruption
Como citar
The Journal of clinical pediatric dentistry, v. 17, n. 4, p. 251-253, 1993.