Cherubism: Clinical case and genetic standpoints
Carregando...
Data
Orientador
Coorientador
Pós-graduação
Curso de graduação
Título da Revista
ISSN da Revista
Título de Volume
Editor
Tipo
Artigo
Direito de acesso
Acesso restrito
Resumo
Cherubism is a rare non-neoplastic hereditary disease, characterized by bilateral bone enlargement of the jaws and is accompanied by inflammation and fibrosis in childhood. An increase in jaw size is noted, with maximum enlargement occurring within 2 years of onset in most cases. By age 7, the lesions become static or progress relatively slowly until puberty. During the late teens, the disease may undergo spontaneous involution. The present case show a patient with history of bilateral enlargement of the jaw with the triad of clinical, histological and radiological findings that helps in the final diagnosis of cherubism.
Descrição
Palavras-chave
Cherubism, Familial, Fibro-osseous disorders, Mandible, Multilocular cystic disease, adolescent, case report, Caucasian, computer assisted tomography, fibrous dysplasia, follow up, histology, human, jaw disease, physical examination, radiodiagnosis
Idioma
Inglês
Citação
Chirurgia, v. 23, n. 5, p. 205-208, 2010.
