Hyaline fibromatosis syndrome: Cutaneous manifestations

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Data

2016-03-01

Autores

Marques, Silvio Alencar [UNESP]
Stolf, Hamilton Ometto [UNESP]
Polizel, Juliana Ocanha [UNESP]
Munhoz, Tânia [UNESP]
Brandão, Marcela Calixto [UNESP]
Marques, Mariangela Esther Alencar [UNESP]

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Resumo

Hyaline fibromatosis syndrome is the current name for clinical manifestations of diseases previously known as “infantile systemic hyalinosis” and “juvenile hyaline fibromatosis”. The authors report representative clinical cases of each one of the above subtypes with emphasis on cutaneous manifestations and difficulties for early diagnosis in this syndrome, essentially of multidisciplinary approach.

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Palavras-chave

Fibroma, Gingival hypertrophy, Mutation, Skin: Skin manifestations

Como citar

Anais Brasileiros de Dermatologia, v. 91, n. 2, p. 226-229, 2016.