EULAR/PRINTO/PRES criteria for Henoch-Schonlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis: Ankara 2008. Part I: Overall methodology and clinical characterisation

dc.contributor.authorRuperto, Nicolino
dc.contributor.authorOzen, Seza
dc.contributor.authorPistorio, Angela
dc.contributor.authorDolezalova, Pavla
dc.contributor.authorBrogan, Paul
dc.contributor.authorCabral, David A.
dc.contributor.authorCuttica, Ruben
dc.contributor.authorKhubchandani, Raju
dc.contributor.authorLovell, Daniel J.
dc.contributor.authorO'Neil, Kathleen M.
dc.contributor.authorQuartier, Pierre
dc.contributor.authorRavelli, Angelo
dc.contributor.authorIusan, Silvia M.
dc.contributor.authorFilocamo, Giovanni
dc.contributor.authorMagalhães, Cláudia Saad [UNESP]
dc.contributor.authorUnsal, Erbil
dc.contributor.authorOliveira, Sheila
dc.contributor.authorBracaglia, Claudia
dc.contributor.authorBagga, Arvind
dc.contributor.authorStanevicha, Valda
dc.contributor.authorManzoni, Silvia Magni
dc.contributor.authorPratsidou, Polyxeni
dc.contributor.authorLepore, Loredana
dc.contributor.authorEspada, Graciela
dc.contributor.authorPaut, Isabelle Kone
dc.contributor.authorZulian, Francesco
dc.contributor.authorBarone, Patrizia
dc.contributor.authorBircan, Zelal
dc.contributor.authordel Rocio Maldonado, Maria
dc.contributor.authorRusso, Ricardo
dc.contributor.authorVilca, Iris
dc.contributor.authorTullus, Kjell
dc.contributor.authorCimaz, Rolando
dc.contributor.authorHorneff, Gerd
dc.contributor.authorAnton, Jordi
dc.contributor.authorGaray, Stella
dc.contributor.authorNielsen, Susan
dc.contributor.authorBarbano, Giancarlo
dc.contributor.authorMartini, Alberto
dc.contributor.institutionUniv Genoa
dc.contributor.institutionHacettepe Univ
dc.contributor.institutionIRCCS G Gaslini
dc.contributor.institutionGen Univ Hosp
dc.contributor.institutionFac Med 1
dc.contributor.institutionGreat Ormond St Hosp Sick Children
dc.contributor.institutionBritish Columbia Childrens Hosp
dc.contributor.institutionHosp Gen Ninos Pedro de Elizalde
dc.contributor.institutionJaslok Hosp
dc.contributor.institutionRes Ctr
dc.contributor.institutionCincinnati Childrens Hosp
dc.contributor.institutionUniversity of Oklahoma
dc.contributor.institutionUniv Paris 05
dc.contributor.institutionHop Necker Enfants Malad
dc.contributor.institutionUniversidade Estadual Paulista (Unesp)
dc.contributor.institutionDokuz EyluL Univ
dc.contributor.institutionUniversidade Federal do Rio de Janeiro (UFRJ)
dc.contributor.institutionOsped Pediat Bambino Gesu
dc.contributor.institutionAll India Inst Med Sci
dc.contributor.institutionRiga Stradins Univ
dc.contributor.institutionIRCCS Policlin S Matteo
dc.contributor.institutionAristotle Univ Thessaloniki
dc.contributor.institutionUniv Trieste
dc.contributor.institutionHNRG Buenos Aires Univ
dc.contributor.institutionSer Pediat Gen
dc.contributor.institutionUniv Padua
dc.contributor.institutionAzienda Policlin Univ Catania
dc.contributor.institutionKocaeli Univ Hosp
dc.contributor.institutionHosp Infantil Mexico Dr Federico Gomez
dc.contributor.institutionHosp Pediat Juan P Garrahan
dc.contributor.institutionOsped A Meyer
dc.contributor.institutionZentrum Allgemeine Paediat & Neonatol
dc.contributor.institutionUniv Barcelona
dc.contributor.institutionHosp Sor Maria Ludovica
dc.contributor.institutionRigshosp
dc.contributor.institutionIRCCS Ist G Gaslini
dc.date.accessioned2014-05-20T13:38:02Z
dc.date.available2014-05-20T13:38:02Z
dc.date.issued2010-05-01
dc.description.abstractObjectives To report methodology and overall clinical, laboratory and radiographic characteristics for Henoch-Schonlein purpura (HSP), childhood polyarteritis nodosa (c-PAN), c-Wegener granulomatosis (c-WG) and c-Takayasu arteritis (c-TA) classification criteria.Methods The preliminary Vienna 2005 consensus conference, which proposed preliminary criteria for paediatric vasculitides, was followed by a EULAR/PRINTO/PRES-supported validation project divided into three main steps. Step 1: retrospective/prospective web-data collection for HSP, c-PAN, c-WG and c-TA, with age at diagnosis <= 18 years. Step 2: blinded classification by consensus panel of a subgroup of 280 cases (128 difficult cases, 152 randomly selected) enabling expert diagnostic verification. Step 3: Ankara 2008 Consensus Conference and statistical evaluation (sensitivity, specificity, area under the curve, kappa-agreement) using as 'gold standard' the final consensus classification or original treating physician diagnosis.Results A total of 1183/1398 (85%) samples collected were available for analysis: 827 HSP, 150 c-PAN, 60 c-WG, 87 c-TA and 59 c-other. Prevalence, signs/symptoms, laboratory, biopsy and imaging reports were consistent with the clinical picture of the four c-vasculitides. A representative subgroup of 280 patients was blinded to the treating physician diagnosis and classified by a consensus panel, with kappa-agreement of 0.96 for HSP (95% CI 0.84 to 1), 0.88 for c-WG (95% CI 0.76 to 0.99), 0.84 for c-TA (95% CI 0.73 to 0.96) and 0.73 for c-PAN (95% CI 0.62 to 0.84), with an overall. of 0.79 (95% CI 0.73 to 0.84).Conclusion EULAR/PRINTO/PRES propose validated classification criteria for HSP, c-PAN, c-WG and c-TA, with substantial/almost perfect agreement with the final consensus classification or original treating physician diagnosis.en
dc.description.affiliationUniv Genoa, PRINTO, IRCCS G Gaslini, EULAR Ctr Excellence Rheumatol, I-16147 Genoa 5, Italy
dc.description.affiliationHacettepe Univ, Childrens Hosp, Ankara, Turkey
dc.description.affiliationIRCCS G Gaslini, Serv Epidemiol & Biostat, Genoa, Italy
dc.description.affiliationGen Univ Hosp, Prague, Czech Republic
dc.description.affiliationFac Med 1, Dept Paediat & Adolescent Med, Prague, Czech Republic
dc.description.affiliationGreat Ormond St Hosp Sick Children, London WC1N 3JH, England
dc.description.affiliationBritish Columbia Childrens Hosp, Vancouver, BC V6H 3V4, Canada
dc.description.affiliationHosp Gen Ninos Pedro de Elizalde, Rheumatol Sect, Buenos Aires, DF, Argentina
dc.description.affiliationJaslok Hosp, Dept Paediat, Mumbai, Maharashtra, India
dc.description.affiliationRes Ctr, Mumbai, Maharashtra, India
dc.description.affiliationCincinnati Childrens Hosp, Med Ctr, Div Rheumatol, Cincinnati, OH USA
dc.description.affiliationUniv Oklahoma, Hlth Sci Ctr, Childrens Hosp OUMC, Oklahoma City, OK USA
dc.description.affiliationUniv Paris 05, Paris, France
dc.description.affiliationHop Necker Enfants Malad, Ctr Reference Natl Arthrites Juveniles, Unite Immunol Hematol & Rhumatol Pediat, Paris, France
dc.description.affiliationUniv Genoa, Dipartimento Pediat, Genoa, Italy
dc.description.affiliationUNESP, Fac Med Botucatu, Hosp Clin, Dept Pediat, Botucatu, SP, Brazil
dc.description.affiliationDokuz EyluL Univ, Fac Med, Div Pediat Rheumatol Immunol, Izmir, Turkey
dc.description.affiliationUniv Fed Rio de Janeiro, Inst Puericultura & Pediat Martagao Gesteira, Rio de Janeiro, Brazil
dc.description.affiliationOsped Pediat Bambino Gesu, Pediat Reumatol IRCCS 2, Rome, Italy
dc.description.affiliationAll India Inst Med Sci, New Delhi 110029, India
dc.description.affiliationRiga Stradins Univ, Riga, Latvia
dc.description.affiliationIRCCS Policlin S Matteo, Pediat Clin, Pavia, Italy
dc.description.affiliationAristotle Univ Thessaloniki, Ippokrat Hosp, Dept Pediat, Ippokrat Gen Hosp, GR-54006 Thessaloniki, Greece
dc.description.affiliationUniv Trieste, Trieste, Italy
dc.description.affiliationHNRG Buenos Aires Univ, Rheumatol Sect, Hosp Ninos Dr Ricardo Gutierrez, Buenos Aires, DF, Argentina
dc.description.affiliationSer Pediat Gen, Ctr Reference Natl Malad Autoinflammatoires, Paris, France
dc.description.affiliationUniv Padua, Dept Pediat, Padua, Italy
dc.description.affiliationAzienda Policlin Univ Catania, Pediat Clin, Catania, Italy
dc.description.affiliationKocaeli Univ Hosp, Kocaeli, Turkey
dc.description.affiliationHosp Infantil Mexico Dr Federico Gomez, Mexico City, DF, Mexico
dc.description.affiliationHosp Pediat Juan P Garrahan, Serv Inmunol Reumatol, Buenos Aires, DF, Argentina
dc.description.affiliationGreat Ormond St Hosp Sick Children, Renal Unit, London WC1N 3JH, England
dc.description.affiliationOsped A Meyer, Dipartimento Pediat, Florence, Italy
dc.description.affiliationZentrum Allgemeine Paediat & Neonatol, St Augustin, Germany
dc.description.affiliationUniv Barcelona, Pediat Rheumatol Unit, Hosp St Joan de Deu, Barcelona, Spain
dc.description.affiliationHosp Sor Maria Ludovica, Unidad Reumatol, La Plata, Buenos Aires, Argentina
dc.description.affiliationRigshosp, Juliane Marie Ctr, Copenhagen, Denmark
dc.description.affiliationIRCCS Ist G Gaslini, Genoa, Italy
dc.description.affiliationUnespUNESP, Fac Med Botucatu, Hosp Clin, Dept Pediat, Botucatu, SP, Brazil
dc.description.sponsorshipEULAR/PRINTO/PRES
dc.format.extent790-797
dc.identifierhttp://dx.doi.org/10.1136/ard.2009.116624
dc.identifier.citationAnnals of The Rheumatic Diseases. London: B M J Publishing Group, v. 69, n. 5, p. 790-797, 2010.
dc.identifier.doi10.1136/ard.2009.116624
dc.identifier.issn0003-4967
dc.identifier.lattes7098310008371632
dc.identifier.orcid0000-0002-7631-7093
dc.identifier.urihttp://hdl.handle.net/11449/13188
dc.identifier.wosWOS:000276982300003
dc.language.isoeng
dc.publisherB M J Publishing Group
dc.relation.ispartofAnnals of the Rheumatic Diseases
dc.relation.ispartofjcr12.350
dc.relation.ispartofsjr7,699
dc.rights.accessRightsAcesso restrito
dc.sourceWeb of Science
dc.titleEULAR/PRINTO/PRES criteria for Henoch-Schonlein purpura, childhood polyarteritis nodosa, childhood Wegener granulomatosis and childhood Takayasu arteritis: Ankara 2008. Part I: Overall methodology and clinical characterisationen
dc.typeArtigo
dcterms.licensehttp://www.bmj.com/about-bmj/resources-authors
dcterms.rightsHolderB M J Publishing Group
unesp.author.lattes7098310008371632[15]
unesp.author.orcid0000-0001-8375-661X[4]
unesp.author.orcid0000-0002-7631-7093[15]
unesp.author.orcid0000-0002-9638-6512[14]
unesp.author.orcid0000-0002-8792-4219[35]
unesp.author.orcid0000-0002-1769-549X[11]
unesp.author.orcid0000-0002-2426-716X[17]
unesp.author.orcid0000-0002-5714-1141[21]
unesp.author.orcid0000-0003-0294-119X[8]
unesp.author.orcid0000-0002-1256-8483[30]
unesp.author.orcid0000-0002-9834-9619[18]
unesp.author.orcid0000-0001-9658-0385[12]
unesp.campusUniversidade Estadual Paulista (Unesp), Faculdade de Medicina, Botucatupt

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