Bone reconstruction and optic functional restoration after fronto-orbital fibrous dysplasia resection

Abstract

Introduction Fibrous dysplasia (FD) is a non-neoplastic developmental hamartomatous disease of the bone in which fibrous tissue gradually expands and replaces normal bone. Case Report An 11-year-old female presented to our maxillofacial service with progressive disturbance of visual acuity and diplopia associated with left forehead prominence mouth with a one-year history of evolution. Computed tomography showed aspect of bone asymmetry with ground-glass appearance. Surgery for removal of her left forehead FD and decompression were performed. The immediate cranio-orbital reconstruction was performed using iliac and calvarium bone grafts and titanium mesh. Histopathological examination demonstrated proliferated fibrous formation in osteoid, which was compatible with fibrous dysplasia. An appropriate restoration of the facial morphology was clinically observed after one year. Her left visual acuity improved with a resolution of the diplopia. Conclusion In conclusion, we report a case of left forehead FD that showed slowly progressive visual symptom. Surgical treatment was effective in the preservation of vision and restoration facial aesthetics.