Calcifilaxia, desafio diagnóstico e terapêutico: Relato de um caso bem sucedido
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Data
2012-09-01
Autores
Roncada, Eduardo Vinicius Mendes
de Abreu, Marilda Aparecida Milanez Morgado
Pereira, Mayra Falcão
de Oliveira, Claúdia Cardoso Macedo
Nai, Gisele Alborghetti [UNESP]
Soares, Deusita Fernandes Gandia
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Resumo
Calciphylaxis, also known as calcific uremic arteriolopathy, is a severe complication often observed in patients with hyperparathyroidism secondary to chronic renal failure, which occurs mainly in women. It is characterized by ischemic tissue loss secondary to progressive vascular compromise. This is a rare and severe condition and its pathogenesis is unclear. The best treatment is prevention, especially in order to maintain adequate levels of calcium and phosphorus. We describe a case of this disease in a patient with hyperparathyroidism secondary to chronic renal failure who underwent medical treatment, surgical debridement and total skin autografts, with resolution of symptoms after 6 months. © 2012 by Anais Brasileiros de Dermatologia.
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Blood vessels, Calcium metabolism disorders, Chronic, Hyperparathyroidism, Ischemia, Renal insufficiency, Secondary
Como citar
Anais Brasileiros de Dermatologia, v. 87, n. 5, p. 752-755, 2012.