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Desafios clínicos e psicossociais no tratamento de um paciente com síndrome de Proteus

dc.contributor.authorBertanha, Matheus [UNESP]
dc.contributor.authorMoura, Regina [UNESP]
dc.contributor.authorSobreira, Marcone Lima [UNESP]
dc.contributor.authorPereira, Lied Martins Santiago [UNESP]
dc.contributor.authorJaldin, Rodrigo Gibin [UNESP]
dc.contributor.authorSegredo, Manuella Pacífico De Freitas [UNESP]
dc.contributor.authorRollo, Hamilton Almeida [UNESP]
dc.contributor.authorYoshida, Winston Bonetti [UNESP]
dc.contributor.institutionUniversidade Estadual Paulista (Unesp)
dc.date.accessioned2018-12-11T16:59:38Z
dc.date.available2018-12-11T16:59:38Z
dc.date.issued2015-10-01
dc.description.abstractProteus syndrome is a rare combination of malformations that can affect several tissues and organs. It is characterized by bilateral macrodactyly, cranial hypertrophy, bone anomalies, scoliosis, soft-tissue hamartomas, verrucous pigmented nevus, visceral abnormalities and other forms of hypertrophy. Just over 200 cases have been reported worldwide. This article reports on the clinical course of a pediatric patient with this syndrome. The child had severe malnutrition associated with extreme gigantism of the lower limbs and also psychosocial problems related to social exclusion. As the disease progressed it exacerbated and evolved into a wasting syndrome. After several years, the parents agreed to amputation of the hypertrophic lower limbs. One year after the amputations the child had been rehabilitated and had adapted to prostheses, with nutritional improvement and notable psychological recovery and social reintegration, which represented a significant improvement in his quality of life.en
dc.description.affiliationUniversidade Estadual Paulista – UNESP Department of Surgery and Orthopedics
dc.description.affiliationUniversidade Estadual Paulista – UNESP Department of Pediatrics
dc.description.affiliationUnespUniversidade Estadual Paulista – UNESP Department of Surgery and Orthopedics
dc.description.affiliationUnespUniversidade Estadual Paulista – UNESP Department of Pediatrics
dc.format.extent346-350
dc.identifierhttp://dx.doi.org/10.1590/1677-5449.005615
dc.identifier.citationJornal Vascular Brasileiro, v. 14, n. 4, p. 346-350, 2015.
dc.identifier.doi10.1590/1677-5449.005615
dc.identifier.fileS1677-54492015000400346.pdf
dc.identifier.issn1677-7301
dc.identifier.issn1677-5449
dc.identifier.lattes9609324832591382
dc.identifier.lattes4513014379461383
dc.identifier.scieloS1677-54492015000400346
dc.identifier.scopus2-s2.0-84949963308
dc.identifier.urihttp://hdl.handle.net/11449/172310
dc.language.isoeng
dc.relation.ispartofJornal Vascular Brasileiro
dc.relation.ispartofsjr0,136
dc.relation.ispartofsjr0,136
dc.rights.accessRightsAcesso aberto
dc.sourceScopus
dc.subjectAmputation
dc.subjectCongenital abnormalities
dc.subjectMusculoskeletal abnormalities
dc.titleDesafios clínicos e psicossociais no tratamento de um paciente com síndrome de Proteuspt
dc.title.alternativeClinical and psychosocial challenges in the treatment of a patient with proteus syndromeen
dc.typeArtigo
dspace.entity.typePublication
unesp.advisor.lattes4513014379461383
unesp.author.lattes9609324832591382
unesp.campusUniversidade Estadual Paulista (UNESP), Faculdade de Medicina, Botucatupt
unesp.departmentCirurgia e Ortopedia - FMBpt

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