Miopatia do multicore: Análise histoquímica de uma família

dc.contributor.authorResende, Luiz Antonio de Lima [UNESP]
dc.contributor.authorKimaid, Paulo André Teixeira [UNESP]
dc.contributor.authorDe Lima Castro, Heloísa Amélia
dc.contributor.authorFonseca, Ronaldo Guimarães [UNESP]
dc.contributor.authorDal Pai, Vitalino [UNESP]
dc.contributor.authorUeda, Anete Kinumi [UNESP]
dc.contributor.authorMontenegro, Mario Rubens Guimarães [UNESP]
dc.contributor.institutionUniversidade Estadual Paulista (Unesp)
dc.contributor.institutionUniversidade Estadual de Campinas (UNICAMP)
dc.date.accessioned2014-05-27T11:19:34Z
dc.date.available2014-05-27T11:19:34Z
dc.date.issued1998-03-01
dc.description.abstractIn this paper the authors describe three cases of multicore myopathy in the same family. Case J was a white 77-year-old patient with proximal muscular atrophy and weakness, global hypotonia and global hypoactive deep tendon reflexes. Motor and sensory conduction studies were normal in all limbs. EMG examination showed a myopathic pattern with frequent spontaneous activity consisting of fibrillations and positive sharp waves. Histochemical reactions showed typical oxidative alterations of multicore myopathy. Cases 2 and 3 were the son and the daughter of case 1 respectively. They were both non-symptomatic patients with minimal EMG and histochemical alterations. These three patients illustrated the great clinical variability of this condition.en
dc.description.affiliationFaculdade de Medicina de Botucatu UNESP
dc.description.affiliationFOP UNICAMP
dc.description.affiliationInstituto de Biocièncias UNESP
dc.description.affiliationUnespFaculdade de Medicina de Botucatu UNESP
dc.description.affiliationUnespInstituto de Biocièncias UNESP
dc.format.extent55-58
dc.identifier.citationRevista Brasileira de Neurologia, v. 34, n. 2, p. 55-58, 1998.
dc.identifier.issn0101-8469
dc.identifier.lattes1346461670550428
dc.identifier.scopus2-s2.0-2542520926
dc.identifier.urihttp://hdl.handle.net/11449/65420
dc.language.isopor
dc.relation.ispartofRevista Brasileira de Neurologia
dc.rights.accessRightsAcesso restrito
dc.sourceScopus
dc.subjectMinicore disease
dc.subjectMulticore disease
dc.subjectMyopathy
dc.titleMiopatia do multicore: Análise histoquímica de uma famíliapt
dc.title.alternativeMulticore disease: Histochemical analysis of a familyen
dc.typeArtigo
unesp.author.lattes1346461670550428
unesp.campusUniversidade Estadual Paulista (Unesp), Faculdade de Medicina, Botucatupt
unesp.departmentNeurologia, Psicologia e Psiquiatria - FMBpt

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